DefinitionPierre Robin syndrome is a condition present at birth, in which the infant has a smaller-than-normal lower jaw, a tongue that falls back in the throat, and difficulty breathing.Alternative NamesRobin sequence; Pierre Robin complex; Pierre Robin anomalyCauses, incidence, and risk factorsThe exact causes of Pierre Robin syndrome are unknown. It may be part of many genetic syndromes.The lower jaw develops slowly before birth, but speeds up during the first year of life.SymptomsCleft soft palateHigh-arched palateJaw that is very small with receding chinJaw placed unusually far back in the throatLarge-appearing tongue compared to jawNatal teeth(teeth appearing when the baby is born)Recurrent ear infectionsSmall opening in the roof of the mouth, which causes chokingSigns and testsA hea