Cori disease (Limit dextrinosis) is caused due to absence of (A) Branching enzyme (B) Debranching enzyme (C) Glycogen synthase (D) Phosphorylase

1 Answer

Answer :

Answer :  B

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Description : Her’s disease is characterized by deficiency of (A) Muscle phosphorylase (B) Liver phosphorylase (C) Debranching enzyme (D) Glycogen synthase

Last Answer : Answer : B

Description : Mc Ardle’s syndrome is characterized by the absence of (A) Liver phosphorylase (B) Muscle phosphorylase (C) Branching enzyme (D) Debranching enzyme

Last Answer : Answer : B

Description : Amylopectinosis is caused due to absence of (A) Debranching enzyme (B) Branching enzyme (C) Acid maltase (D) Glucose-6-phosphatase

Last Answer : Answer : B

Description : Amylo 1, 6 glucosidase is called (A) Branching enzyme (B) debranching enzyme (C) Glucantransferase (D) Phosphorylase

Last Answer : B

Description : Glycogen is converted to glucose-1- phosphate by (A) UDPG transferase (B) Branching enzyme (C) Phosphorylase (D) Phosphatase

Last Answer : C

Description : One of the following enzymes does not change glycogen synthase a to b. (A) Glycogen synthase kinases 3, 4, 5 (B) Ca2+ calmodulin phosphorylase kinase (C) Ca2+ calmodulin dependent protein kinase (D) Glycogen phosphorylase a

Last Answer : D

Description : Pompe ’s d isease is caused due to deficiency of (A) Lysosomal α-1→4 and 1→6-glucosidase (B) Glucose-6-phosphatase (C) Glycogen synthase (D) Phosphofructokinase

Last Answer : Answer : A

Description : In glycogenesis a branch point in the molecule is established by the enzyme (A) Amylo[1→ 4][1→ 6] transglucosidase (B) α [1→ 4] α [1→ 4] Glucan transferase (C) Amylo [1→ 6] glucosidase (D) Glycogen synthase

Last Answer : Answer : A

Description : A regulator of the enzyme Glycogen synthase is (A) Citric acid (B) 2, 3 bisphosphoglycerate (C) Pyruvate (D) GTP

Last Answer : C

Description : The branching enzyme acts on the glycogen when the glycogen chain has been lengthened to between glucose units: (A) 1 and 6 (B) 2 and 7 (C) 3 and 9 (D) 6 and 11

Last Answer : D

Description : Debranching enzyme is absent in (A) Cori’s disease (B) Andersen’s disease (C) Von Gierke’s disease (D) Her’s disease

Last Answer : A

Description : After the action of phosphorylase, glycogen is converted into (A) Amylopectin (B) dextrin (C) Amylose (D) Maltose

Last Answer : Answer : B

Description : Glycogen phosphorylase liberates the following from glycogen (A) Glucose (B) Glucose-6-phosphate (C) Glucose-1-phosphate (D) Maltose

Last Answer : Answer : C

Description : Pyridoxal phosphate is a coenzyme for (A) Glycogen synthetase (B) Phosphorylase (C) Both (A) and (B) (D) None of these

Last Answer : Answer : B

Description : Glycogen while being acted upon by active phosphorylase is converted first to (A) Glucose (B) Glucose 1-phosphate and Glycogen with 1 carbon less (C) Glucose-6-phosphate and Glycogen with 1 carbon less (D) 6-Phosphogluconic acid

Last Answer : C

Description : What will activate glycogen phosphorylase?

Last Answer : Epinephrine, glucagon, cyclic AMP.

Description : Tarui disease is characterized by the deficiency of the enzyme: (A) Liver phosphorylase (B) Muscle phosphorylase (C) Muscle and erythrocyte phosphofructokinase (D) Lysosomal acid maltase

Last Answer : Answer : C

Description : The hormone activating the glycogen synthase activity is (A) Insulin (B) Glucagon (C) Epinephrine (D) ACTH

Last Answer : Answer : A

Description : Action of glycogen synthase is inhibited by (A) Insulin (B) Glucose (C) Mg2+ (D) Cyclic AMP

Last Answer : Answer : C

Description : Allosteric activator of glycogen synthase is (A) Glucose (B) Glucose-6-Phosphate (C) UTP (D) Glucose-1-phosphate

Last Answer : Answer : B

Description : One of the following statement is correct: (A) Glycogen synthase ‘a’ is the phosphorylated (B) cAMP converts glycogen synthase b to ‘a’ (C) Insulin converts glycogen synthase b to a (D) UDP glucose molecules interact and grow into a Glycogen tree

Last Answer : C

Description : Branching occurs in glycogen approximately after every (A) Five glucose units (B) Ten glucose units (C) Fifteen glucose units (D) Twenty glucose units

Last Answer : B

Description : Pyridoxal phosphate is a coenzyme for (A) Glycogen synthetase (B) Phosphorylase (C) Both (A) and (B) (D) None of these

Last Answer : (B) Phosphorylase

Description : McArdle’s disease is due to the deficiency of (A) Glucose-6-phosphatase (B) Phosphofructokinase (C) Liver phosphorylase (D) muscle phosphorylase

Last Answer : D

Description : Hereditary coproporphyria is caused due to deficiency of (A) Protoporphyrinogen oxidase (B) ALA synthase (C) ALA dehydratase (D) Coproporphyrinogen oxidase

Last Answer : Answer : D

Description : Acute intermittent porphyria (paraoxymal porphyria) is caused due to deficiency of (A) Uroporphyrinogen I synthase (B) ALA synthase (C) Coproporphyrinogen oxidase (D) Uroporphyrinogen decarboxylase

Last Answer : Answer : A

Description : Which is the defective enzyme in von Gierkeís disease (glycogen storage disease type I)? 

Last Answer : Glucose-6-phosphatase.

Description : The enzyme common to catabolism of all the purines is (A) Adenosine deaminase (B) Purine nucleoside phosphorylase (C) Guanase (D) None of these

Last Answer : Answer : B

Description : The enzyme that converts glucose to glucose-6-phosphate is (A) Phosphatase (B) Hexokinase (C) Phosphorylase (D) Glucose synthetase

Last Answer : Answer : B

Description : In glycogenolysis, the enzyme which transfers a trisaccharide unit from one branch to the other exposing 1→ 6 branch point is (A) Phosphorylase (B) α-[1→ 4]→ α-[1→ 4]→ Glucan transferase (C) Amylo [1→ 6] glucosidase (D) Amylo[1→ 4]→ [1→ 6] transglucosidase

Last Answer : Answer : B

Description : The following enzyme is required for the hexose monophosphate shunt pathway: (A) Glucose-6-phosphatase (B) Phosphorylase (C) Aldolase (D) Glucose-6-phosphate dehydrogenase

Last Answer : D

Description : The enzyme involved in congenial erythropoietic porphyria is (A) Uroporphyrinogen I synthase (B) Uroporphyrinogen III cosynthase (C) Protoporphyrinogen oxidase (D) Ferrochelatase

Last Answer : Answer : B

Description : The synthesis of heme from protophyrin III is catalysed by the enzyme: (A) ALA synthase (B) Ferroreductase (C) Ferrooxidase (D) Ferrochelatase

Last Answer : Answer : D

Description : In mammalian liver the rate controlling enzyme in porphyrin biosynthesis is (A) ALA synthase (B) ALA hydratase (C) Uroporphyrinogen I synthase (D) Uroporphyrinogen III cosynthase

Last Answer : Answer : A

Description : A regulator of the enzyme glucogen synthase is (A) Citric Acid (B) Pyruvate (C) Glucose-6-PO4 (D) GTP

Last Answer : Answer : C

Description : The protein, which is in fact a multifunctional enzyme complex in higher organism is (A) Acetyl transacylase (B) Malonyl transacylase (C) 3-Hydroxy acyl-ACP dehyratase (D) Fatty acid synthase

Last Answer : Answer : D

Description : The enzyme acyl-CoA synthase catalyses the conversion of a fatty acid of an active fatty acid in the presence of (A) AMP (B) ADP (C) ATP (D) GTP

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Description : Cori cycle is (A) Synthesis of glucose (B) reuse of glucose (C) uptake of glycose (D) Both (A) & (B)

Last Answer : D

Description : Taenia saginata differs from Taenia solium in (a) absence of scolex hooks (b) absence of scolex hooks and uterine branching (c) absence of scolex hooks and presence of both male and female reproductive organs (d) presence of scolex hooks.

Last Answer : (a) absence of scolex hooks

Description : Von Gierke’s disease is characterized by the deficiency of (A) Glucose-6-phosphatase (B) α -1→ 4 Glucosidase (C) 1→ 6 Glucosidase (D) Liver phosphorylase

Last Answer : Answer : A

Description : Galactosemia is due the absence of which enzyme?

Last Answer : Galactose-1-phosphate uridyl transferase. 

Description : Insulin has no effect on the activity of the enzyme: (A) Glycogen synthetase (B) Fructokinase (C) Pyruvate kinase (D) Pyruvate dehydrogenase

Last Answer : Answer : B

Description : In the TCA cycle, at which of the following enzyme-catalyzed steps, incorporation of elements of water into an intermediate of the cycle takes place : (A) Citrate synthase (B) Aconitase (C) Maleate dehydrogenase (D) Succinyl Co-A synthase

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Description : cori cycle involves

Last Answer : cori cycle involves A. Liver B. Muscles C. Liver and muscles both D. None the these

Description : In ureotelic animals, urea is formed by (a) Krebs’ cycle (b) EM pathway (c) Ornithine cycle (d) Cori cycle.

Last Answer : (c) Ornithine cycle

Description : The current carrying capacity of cables in D.C. is more that in A.C. mainly due to (a) absence of harmonics (b) non-existence of any stability limit (c) smaller dielectric loss (d) absence of ripples (e) none of the above

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Description : Pick out the wrong statement. (A) Linear polymers are formed from bifunctional groups only and are normally thermoplastic (B) Cross-linked branched chain polymers are either elastometric or ... (D) Dibasic acids reacts with dihydric alcohols to give polyesters using addition polymerisation reaction

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Description : Hereditary fructose intolerance involves the absence of the enzyme: (A) Aldalose B (B) Fructokinase (C) Triokinase (D) Phosphotriose isomerase

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Description : The α-ketoacid is decarboxylated by H2O2 forming a carboxylic acid with one carbon atom less in the absence of the enzyme: (A) Catalase (B) Decarboxylase (C) Deaminase (D) Phosphatase

Last Answer : Answer : A